Online ISSN: 1303-6289
Print ISSN: 0304-4793


Published Online: 
February 8, 2010


 

Turkish Archives of Otolaryngology (Online Preprint Issue) Abstract




Full Text in Turkish [PDF] 167 KB


 

 

 

 

Mondini and Michel deformitites of the inner ear: a case report

Caglar Calli*, Ercan Pinar*, Semih Oncel*, A. Kadir Imre*, Melda Apaydin**


*3rd Clinic of ENT, and **Department of Radiology, Ataturk Research and Training Hospital, Izmir, Turkey
Key Words

Michel aplasia, Mondini dysplasia, congenital hearing loss
Abstract

 

 

 

Congenital hearing loss is an important disease in otology. Approximately 20 percent of congenital sensorineural hearing loss have radiological bone malformations. Inner ear anomalies, resulting in congenital sensorineural hearing loss, observation frequency are classified according to Schuknecht: Mondini, Scheibe, Michel and Alexander. These malformations are rare and occur due to stoppage of development of inner ear, in the first trimester of pregnancy. In our case, eigth-years-old patient referred us with congenital hearing loss at right ear and effusion at left ear following common cold. After evaluation of the patient, we determined the Michel aplasia and Mondini dysplasia together. A case study with diagnosis and management together with relevant literature study is presented in this article.

doi:10.2399/tao.06.027

Received:  October 19, 2006
Accepted after revision:  August 19, 2009
Correspondence: Caglar Calli, MD 
1394 Sok. 7/1 Birlik Apt. D. 1
Alsancak, Izmir, Turkey
Phone: +90 232 421 57 57
e-mail: caglarcalli@hotmail.com

   
   


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